macrodystrophia lipomatosa: ct and m r findings

macrodystrophia lipomatosa is a rare congenital form of localized gigantism characterized by an increase in all mesenchymal elements, particularly fibroadipose tissue. mr imaging can be used to examine the soft tissue and detect the fibrous and fatty hypertrophy that characterizes this condition and also diagnose an associated fibrolipomatous hamartoma of the median or plantar nerve. we describe the clinical and radiological findings (including ct scan, mri and bone scan) and also progression of this rare entity during a 10 year period.